Ectodermal Dysplasia Syndrome withOrthodontic Treatment and Oral Finds: A CaseReport

نویسندگان

  • Weihao Li
  • Yanhua Xu
  • Song Li
چکیده

Ectodermal dysplasia, which affects ectodemal derivatives, currently is an X-linked recessive inheritary hypohydrotic ectodermal dysplasia. Patients with ectodermal dysplasia usually characterized by congenital teeth loss, abnormal teeth and inherited through female carriers. In this case report, we present a 5 years old boy of China ethnicity with mandibular anodontia, a rare dental dysplasia in ectodermal dysplasia syndrome. To compromise esthetics and function, a multidisciplinary approach was performed by oral physician, oral pathologist, orthodontist and prosthodontist.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

سندرم Ectrodactyly– ectodermal dysplasia clefting: گزارش مورد به همراه علائم دهانی

  Objectives: Ectrodactyly-ectodermal dysplasia-clefting syndrome (EEC) is a rare syndrome with features of ectrodactyly, ectodermal dysplasia and cleft lip/palate. This study presents an Iranian case with classic features and oral complications.   Case: We report a 20-year old female with all manifestations of this syndrome. The simultaneous presence of these three malformations is extremely r...

متن کامل

Ellis-van Creveld with an Unusual Dental Anomaly: A Case Report

The Ellis-van Creveld (EVC) syndrome is a chondroectodermal dysplasia and is characterized by the cardinal features of disproportionate short stature, polydactyly, hidrotic ectodermal dysplasia, and congenital heart malformations, along with other skeletal and dental abnormalities. It is a rare condition, with very few cases reported in the medical literature. It is inherited as an autosomal re...

متن کامل

Complications of Implant Rehabilitation in Ectodermal Dysplasia Patients: A Review Study

Background and Aim: Ectodermal dysplasia (ED) is a hereditary disease that affects ectodermal tissues. Its oral manifestations include hypodontia or oligodontia, which cause the reduction of the height and width of the alveolar ridge. Considering numerous difficulties that these patients encounter with regard to facial appearance, talking, and chewing, their rehabilitation has a major influence...

متن کامل

Chondroectodermal dysplasia (Ellis-Van Creveld syndrome: A case report

Ellis-Van Creveld syndrome is a very rare congenital disorder which its principal features are polysyndactyly, chondrodysplasia, cardiac abnormalities and ectodermal dysplasia. We report a 10-year-old girl with major manifestations of this syndrome who also had multiple brownish macules and patches on trunk and extremities with aortic and pulmonary stenosis in echocardiographic evaluations.

متن کامل

Dental Management of Ectodermal Dysplasia Syndrome at an Early Age: A Case Report

Objectives: Ectodermal dysplasia (ED) is a relatively common sex-linked dermatitis characterized by congenital dysplasia of one or more ectodermal structures and their accessory appendages. Common manifestations include fragile skin and nails, defective teeth and salivary glands, frontal bossing with prominent supra orbital ridges, nasal bridge depression and protuberant lips. Teeth are often f...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره   شماره 

صفحات  -

تاریخ انتشار 2017